Orbital lymphangiomas are congenital lesions that can affect any part of the body, including the periocular region. They are benign lesions that are usually present from birth, although they may go unnoticed until they manifest years later.
These orbital lymphangiomas are composed of dilated lymphatic ducts and cavities filled with fluid. They are space-occupying orbital tumors, so when they appear in the eye socket, they pose a significant problem, as the orbit does not have “extra” space to expand, and the lesion can affect the structures responsible for vision.